Behçet’s Disease Presenting with Cerebellar Involvement

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Catarina Machado - Corresponding Author

Catarina Machado [catarinamachado.med@gmail.com]
Rua Conceição Fernandes, 4434-502, Vila Nova de Gaia, Portugal

Maria Ana Canelas
Pedro Barros
Luís Andrade
Carina Silva
Vítor P. Dias

Abstract

Behçet’s disease is a rare multisystemic vasculitis that most commonly presents with recurrent episodes of oral ulceration. However, other system involvement may be the first sign. We report a case of a 45-year-old male who presented with walking instability, loss of motor/sensory function on the upper left arm, vertigo and poor visual acuity. The magnetic resonance imaging showed an expansive lesion in the posterior fossa adjacent to the middle cerebellar peduncle. On ophthalmic examination, he presented occlusion of the inferior temporal vein. After a complete anamnesis, it was possible to establish a history of recurrent aphthous ulceration in the oral mucosa. Due to high suspicion of Behçet’s disease with neurological involvement, the patient was started on corticosteroids, with clinical, analytical and imagiologic improvement. Behçet’s disease can be very difficult to diagnose when the initial manifestation does not include the classic clinical triade of oral aphthous ulceration, genital ulcers and ocular disease.

Keywords: Behcet Syndrome; Nervous System Diseases

Article Details

1.
Machado C, Canelas MA, Barros P, Andrade L, Silva C, Dias VP. Behçet’s Disease Presenting with Cerebellar Involvement. Gaz Med [Internet]. 2020 Sep. 30 [cited 2024 Nov. 24];7(3). Available from: https://gazetamedica.pt/index.php/gazeta/article/view/269
Section
CLINICAL CASE